HYPEREOSINOPHILIC CARDIOMYOPATHY WITH NON-COMPACTION FEATURES COMPLICATED BY MID LV CAVITY OBSTRUCTION: A CASE REPORT

Abstracts

Cardiomyopathies represent a wide spectrum of myocardial disease where each type of cardiomyopathy have distinctive morphological features, the overlap between 2 distinct types of cardiomyopathies is rare, we are describing a case of  hypereosinophilic cardiomyopathy where the morphological features of both ventricles simulate non compaction cardiomyopathy and hypereosinophilic cardiomyopathy .although the non-compaction features are not typical the overlap between the cardiomyopathies caused an unusual myocardial morphology .the endocardial fibrosis progressed to form a fibrous endocardial mid left ventricular ring that caused significant mid LV obstruction ,the severe LV obstruction progressed to biventricular failure .the patient was referred to surgery to relieve the obstruction with improvement in his NYHA class and LV functions after the operation .this case highlights the possibility of having atypical myocardial features that cannot fit in one type of myocardial disease, it also shows a severe progressive form of endocardial fibrosis to the extent of causing severe LV obstruction.

Keywords : Hypereosinophilic cardiomyopathy; left ventricular mid cavity obstruction; LV non compaction.

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